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KMID : 0985520180230030127
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Korean Journal of Pancreas and Biliary Tract
2018 Volume.23 No. 3 p.127 ~ p.133
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A 2-Week Steroid Trial for Differentiating Isolated IgG4-Related Sclerosing Cholangitis from Cholangiocarcinoma
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Lee Bho-Hyeon
Moon Sung-Hoon
Min Kyueng-Whan
Park Ji-Won
Lim Hyun
Kim Sung-Eun
Kang Ho-Suk
Kim Jong-Hyeok
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Abstract
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Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is rare disease which is steroid-responsive and often associated with IgG4 related systemic disease such as autoimmune pancreatitis. It is characterized by increased serum IgG4 and IgG4-positive lymphoplasmacytic infiltration in bile ducts. It is often difficult to distinguish IgG4-SC to hilar cholangiocarcinoma if it manifests as an isolated bile duct. We report a case of 79-year-old woman with IgG4-SC which was difficult to distinguish hilar cholangiocarcinoma due to similar clinical and radiologic findings, showing good therapeutic effect after a 2-week steroid trial.
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KEYWORD
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Immunoglobulin G4, Sclerosing cholangitis, Steroid, Cholangiocarcinoma
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